Exstrophy of cloaca sequence

Exstrophy of cloaca sequence is a rare congenital anomaly with an incidence of (1/200,000), and includes a variety of malformations in the caudal region of the trunk. The major presenting defect is exstrophied of the caecum lying between two exstrophied halves of the bladder. We report a case of exstrophy of cloaca sequence that was associated with omphalocele, meningocele, hip dislocation, imperforate anus and lower extremity anomalies. The parents refused any surgical reconstruction and the baby died on the 36th day of life, presumably due to malnutrition and dehydration.