2026-08-252026-08-25https://scholars.csmu.edu.tw/handle/123456789/17049Myotonic dystrophy type 1 (DM1) is a multisystemic dominant disease caused by expansion of CUG repeats in the 3’-UTR of the DMPK gene. In DM cells, the MBNL proteins are sequestered by CUG repeats...(詳)肌強直肌肉形萎縮症(Myotonic dystrophy type I),簡稱DM1,是屬於多系統性神經肌肉退化性疾病的一種單基因顯性的遺傳疾病,DM1 病人的致病機制是在DMPK 基因的3’...(詳)強直型肌肉萎縮症第一型(DM1)CUG擴增MBNL1抑制miRNAmyoDC2C12肌母細胞肌細胞分化myotonic dystrophy type 1(DM1)CUG expansionMBNL1 knockdownmiRNAmyoDC2C12 myoblastsmyogenic differentiation探討miRNA參與在CUG重複序列擴增及MBNL1 knockdown抑制肌纖維母細胞分化的角色research project